Pediatric Langerhans Cell Histiocytosis Presenting With Bilateral Parotid Gland Swelling and Cystic Lung Disease

Langerhans cell histiocytosis (LCH) is a neoplastic process originating from immature myeloid precursor cells. In this report, we describe a case of a 17-month-old with scaling of the scalp and swelling of the bilateral parotid glands who developed acute respiratory distress. Evaluation revealed extensive pulmonary involvement, and a skin biopsy was found to be consistent with LCH. Pediatric LCH rarely presents with bilateral parotid gland involvement or cystic lung disease, emphasizing the importance of comprehensive evaluation of pediatric patients with LCH.

Abstract from PubMed